SKIP005847 : LHON1-hiPSC5

Cell Line NameLHON1-hiPSC5
Original Database URL
Database
Cell Line Name(2)RSCB0130
SpeciesHuman
TypeiPS Cell
Original TissueSkin Dermal Fibroblast
Disease StatusDiseased
Description
Cell Morphologyhuman ES-like
Grade--

Method for Establishment

VectorRetrovirus
Feeder CellYesInactivated Mouse Embryonic Fibroblast (MEF, NMRI strain, Inactivation by Mitomycin C, Sigma, M0503)/ or Matrigel (Sigma, E1270)
MediumDMEM/F12 medium (Gibco, cat# 21331020) supplemented with 20% Knock-out Serum (Gibco, cat# 10828028), 2 mM L-glutamine
CO2(%)5%

Detection of Contaminants

Mycoplasma Negative Method

Pluripotency Tests

Pluripotent MarkersYes Assay
in vitro DifferentiationYes Assay
in vivo DifferentiationYes Assay

Chromosomal QC

KaryotypeYes Assay

No data available
Disease NameLeber's Hereditary Optic NeuropathyICD10
OMIM ID
Age48
SexMale
RaceAsian
Genetic Analysis No
No data available

Contact Information

# Name Organization Contact Email
1 Professor Hossein Baharvand Royan Stem cell Bank, Iran

Provider/Distributor

# Availability Organization Email URL
1 Not Available Royan Stem cell Bank, Iran https://www.royaninstitute.org/